{"product_id":"nsj-r32602-100ug","title":"Gla Antibody \/ Galactosidase alpha, 100 ug","description":"\u003cp\u003eAlpha-galactosidase is a glycoside hydrolase enzyme that encoded by the GLA gene. This gene is a homodimeric glycoprotein that hydrolyses the terminal alpha-galactosyl moieties from glycolipids and glycoproteins. This enzyme predominantly hydrolyzes ceramide trihexoside, and it can catalyze the hydrolysis of melibiose into galactose and glucose. A variety of mutations in this gene affect the synthesis, processing, and stability of this enzyme, which causes Fabry disease, a rare lysosomal storage disorder that results from a failure to catabolize alpha-D-galactosyl glycolipid moieties.\u003c\/p\u003e","brand":"NSJ Bioreagents","offers":[{"title":"100 ug","offer_id":48536506302688,"sku":"R32602","price":449.0,"currency_code":"KRW","in_stock":true}],"thumbnail_url":"\/\/cdn.shopify.com\/s\/files\/1\/0601\/9330\/8896\/files\/get_image_a71fc313-3a9d-4aeb-acbb-311feadec1fd.jpg?v=1768310678","url":"https:\/\/rndmate.com\/products\/nsj-r32602-100ug","provider":"알앤디메이트","version":"1.0","type":"link"}